a congenital condition characterized by a port wine stain, usually on one side of the face, and a hemangioma on the brain. May also include seizures, glaucoma, developmental delays, and enlarging of the eye on the side of the port wine stain.
Sturge-Weber syndrome (SWS) is a disorder involving the association of a facial port-wine stain with glaucoma and abnormal blood vessels called a leptomeningeal angioma on the surface of the brain. The facial port-wine stain is present from birth and when it ocurrs on the forehead and/or upper eyelid (ophthalmic distribution) is associated with an increased risk (10-20%) of the full syndrome. SWS can involve one side of the head (unilateral) or both sides (bilateral). Infants with Sturge-Weber Syndrome are at increased risk of developing, epilepsy, developmental delays, mental retardation, weakness on a side of the body (hemiparesis), and vision loss.
A disorder of blood vessels affecting the skin of the face, eyes, and brain; brain involvement is associated with seizures.